List of works - Marie-Agnès Dragon-Durey

Genetics and outcome of atypical hemolytic uremic syndrome: a nationwide French series comparing children and adults

scientific article

Anti-Factor H autoantibodies associated with atypical hemolytic uremic syndrome

scientific article

Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies

scientific article published on 28 March 2012

Mutations in complement C3 predispose to development of atypical hemolytic uremic syndrome

scientific article

Differential impact of complement mutations on clinical characteristics in atypical hemolytic uremic syndrome

scientific article

Complement factor I: a susceptibility gene for atypical haemolytic uraemic syndrome

scientific article

Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases

scientific article

Genetic and functional analyses of membrane cofactor protein (CD46) mutations in atypical hemolytic uremic syndrome

scientific article

Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome

scientific article

Pregnancy-associated hemolytic uremic syndrome revisited in the era of complement gene mutations

scientific article

Mutations in components of complement influence the outcome of Factor I-associated atypical hemolytic uremic syndrome

scientific article

Inhibition of the mTORC pathway in the antiphospholipid syndrome

scientific article

Prompt plasma exchanges and immunosuppressive treatment improves the outcomes of anti-factor H autoantibody-associated hemolytic uremic syndrome in children

scientific article

Atypical aHUS: State of the art.

scientific article

Alternative complement pathway assessment in patients with atypical HUS.

scientific article

Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome

scientific article

The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome.

scientific article

A prevalent C3 mutation in aHUS patients causes a direct C3 convertase gain of function

scientific article

Y402H complement factor H polymorphism associated with exudative age-related macular degeneration in the French population

article

Overall neutralization of complement factor H by autoantibodies in the acute phase of the autoimmune form of atypical hemolytic uremic syndrome

scientific article

Atypical hemolytic uremic syndrome associated with complement factor H autoantibodies and CFHR1/CFHR3 deficiency

scientific article

Successful pre-transplant management of a patient with anti-factor H autoantibodies-associated haemolytic uraemic syndrome

scientific article

Atypical haemolytic uraemic syndrome and mutations in complement regulator genes

scientific article

An engineered construct combining complement regulatory and surface-recognition domains represents a minimal-size functional factor H.

scientific article

Anti-factor H autoantibodies in C3 glomerulopathies and in atypical hemolytic uremic syndrome: one target, two diseases

scientific article

Autoantibodies in haemolytic uraemic syndrome (HUS).

scientific article

Anti-factor H autoantibody-associated hemolytic uremic syndrome: review of literature of the autoimmune form of HUS.

scientific article

Anti-Factor H autoantibodies in a fifth renal transplant recipient with atypical hemolytic and uremic syndrome.

scientific article

Pulse cyclophosphamide therapy and clinical remission in atypical hemolytic uremic syndrome with anti-complement factor H autoantibodies

scientific article

Standardisation of the factor H autoantibody assay

scientific article

Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses

scientific article

C5 nephritic factors drive the biological phenotype of C3 glomerulopathies

scientific article published on 14 July 2017

Varicella as a trigger of atypical haemolytic uraemic syndrome associated with complement dysfunction: two cases

scientific article

Autoantibodies against complement components and functional consequences.

scientific article published on 20 June 2013

Heterogeneous pattern of renal disease associated with homozygous Factor H deficiency

scientific article published on 10 March 2011

Prevalence of monoclonal gammopathy in patients presenting with acquired angioedema type 2

scientific article published on 01 August 2002

Functional Characterization of Autoantibodies against Complement Component C3 in Patients with Lupus Nephritis.

scientific article

A case of C3 glomerulonephritis successfully treated with eculizumab

scientific article published on 22 March 2015

Effect of plasma exchange and immunosuppressive medications on antibody titers and outcome in anti-complement factor H antibody-associated hemolytic uremic syndrome

scientific article published on September 13, 2014

Genetics of hemolytic uremic syndromes

scientific article

Functional evaluation of factor H genetic and acquired abnormalities: application for atypical hemolytic uremic syndrome (aHUS).

scientific article

Unusual clinical severity of complement membrane cofactor protein-associated hemolytic-uremic syndrome and uniparental isodisomy

scientific article

A novel CFHR1-CFHR5 hybrid leads to a familial dominant C3 glomerulopathy.

scientific article published on 17 July 2017

Expression of low-affinity Fc gamma receptor by a human metastatic melanoma line.

scientific article

Atypical hemolytic-uremic syndrome related to abnormalities within the complement system

scientific article

Application of Deamidated Gliadin Antibodies in the Follow-Up of Treated Celiac Disease.

scientific article published on 31 August 2015

Déficits en protéines du complément en pathologie humaine

scientific article published on 01 May 2006

Lupus nephritis associated with complete C1s deficiency efficiently treated with rituximab: A case report

scientific article published on 01 September 2010

Non-Hodgkin’s lymphomas and myeloid disorders: deletions associated with t(2;5) and t(3;5) detected by FISH

scientific article published on 01 July 1998

Hereditary angio-oedema: effective treatment with the progestogen-only pill in a young woman.

scientific article published in September 2004

List of works by Marie-Agnès Dragon-Durey

Genetics and outcome of atypical hemolytic uremic syndrome: a nationwide French series comparing children and adults

Anti-Factor H autoantibodies associated with atypical hemolytic uremic syndrome

Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies

Mutations in complement C3 predispose to development of atypical hemolytic uremic syndrome

Differential impact of complement mutations on clinical characteristics in atypical hemolytic uremic syndrome

Complement factor I: a susceptibility gene for atypical haemolytic uraemic syndrome

Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases

Genetic and functional analyses of membrane cofactor protein (CD46) mutations in atypical hemolytic uremic syndrome

Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome

Pregnancy-associated hemolytic uremic syndrome revisited in the era of complement gene mutations

Mutations in components of complement influence the outcome of Factor I-associated atypical hemolytic uremic syndrome

Inhibition of the mTORC pathway in the antiphospholipid syndrome

Prompt plasma exchanges and immunosuppressive treatment improves the outcomes of anti-factor H autoantibody-associated hemolytic uremic syndrome in children

Atypical aHUS: State of the art.

Alternative complement pathway assessment in patients with atypical HUS.

Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome

The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome.

A prevalent C3 mutation in aHUS patients causes a direct C3 convertase gain of function

Y402H complement factor H polymorphism associated with exudative age-related macular degeneration in the French population

Overall neutralization of complement factor H by autoantibodies in the acute phase of the autoimmune form of atypical hemolytic uremic syndrome

Atypical hemolytic uremic syndrome associated with complement factor H autoantibodies and CFHR1/CFHR3 deficiency

Successful pre-transplant management of a patient with anti-factor H autoantibodies-associated haemolytic uraemic syndrome

Atypical haemolytic uraemic syndrome and mutations in complement regulator genes

An engineered construct combining complement regulatory and surface-recognition domains represents a minimal-size functional factor H.

Anti-factor H autoantibodies in C3 glomerulopathies and in atypical hemolytic uremic syndrome: one target, two diseases

Autoantibodies in haemolytic uraemic syndrome (HUS).

Anti-factor H autoantibody-associated hemolytic uremic syndrome: review of literature of the autoimmune form of HUS.

Anti-Factor H autoantibodies in a fifth renal transplant recipient with atypical hemolytic and uremic syndrome.

Pulse cyclophosphamide therapy and clinical remission in atypical hemolytic uremic syndrome with anti-complement factor H autoantibodies

Standardisation of the factor H autoantibody assay

Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses

C5 nephritic factors drive the biological phenotype of C3 glomerulopathies

Varicella as a trigger of atypical haemolytic uraemic syndrome associated with complement dysfunction: two cases

Autoantibodies against complement components and functional consequences.

Heterogeneous pattern of renal disease associated with homozygous Factor H deficiency

Prevalence of monoclonal gammopathy in patients presenting with acquired angioedema type 2

Functional Characterization of Autoantibodies against Complement Component C3 in Patients with Lupus Nephritis.

A case of C3 glomerulonephritis successfully treated with eculizumab

Effect of plasma exchange and immunosuppressive medications on antibody titers and outcome in anti-complement factor H antibody-associated hemolytic uremic syndrome

Genetics of hemolytic uremic syndromes

Functional evaluation of factor H genetic and acquired abnormalities: application for atypical hemolytic uremic syndrome (aHUS).

Unusual clinical severity of complement membrane cofactor protein-associated hemolytic-uremic syndrome and uniparental isodisomy

A novel CFHR1-CFHR5 hybrid leads to a familial dominant C3 glomerulopathy.

Expression of low-affinity Fc gamma receptor by a human metastatic melanoma line.

Atypical hemolytic-uremic syndrome related to abnormalities within the complement system

Application of Deamidated Gliadin Antibodies in the Follow-Up of Treated Celiac Disease.

Déficits en protéines du complément en pathologie humaine

Lupus nephritis associated with complete C1s deficiency efficiently treated with rituximab: A case report

Non-Hodgkin’s lymphomas and myeloid disorders: deletions associated with t(2;5) and t(3;5) detected by FISH

Hereditary angio-oedema: effective treatment with the progestogen-only pill in a young woman.