List of works - José Antonio Enríquez

Mitochondrial cristae shape determines respiratory chain supercomplexes assembly and respiratory efficiency

scientific article published on 19 September 2013

Respiratory active mitochondrial supercomplexes.

scientific article

Supercomplex assembly determines electron flux in the mitochondrial electron transport chain

scientific article

Respiratory complex III is required to maintain complex I in mammalian mitochondria

scientific article

Human mtDNA haplogroups associated with high or reduced spermatozoa motility

scientific article

Differences in reactive oxygen species production explain the phenotypes associated with common mouse mitochondrial DNA variants

scientific article published on October 2006

MtDNA mutation in MERRF syndrome causes defective aminoacylation of tRNA(Lys) and premature translation termination

scientific article published in May 1995

NDUFA4 Is a Subunit of Complex IV of the Mammalian Electron Transport Chain

scientific article published on August 16, 2012

Mitochondrial Cristae: Where Beauty Meets Functionality.

scientific article published on 5 February 2016

Loss of mitochondrial protease OMA1 alters processing of the GTPase OPA1 and causes obesity and defective thermogenesis in mice

scientific article

Induction of the mitochondrial NDUFA4L2 protein by HIF-1α decreases oxygen consumption by inhibiting Complex I activity.

scientific article

Mitochondrial and nuclear DNA matching shapes metabolism and healthy ageing.

scientific article published on 6 July 2016

Isolation of biogenetically competent mitochondria from mammalian tissues and cultured cells

scientific article

The deafness-associated mitochondrial DNA mutation at position 7445, which affects tRNASer(UCN) precursor processing, has long-range effects on NADH dehydrogenase subunit ND6 gene expression.

scientific article

The mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episode syndrome-associated human mitochondrial tRNALeu(UUR) mutation causes aminoacylation deficiency and concomitant reduced association of mRNA with ribosomes.

scientific article

Mitochondrial ROS Produced via Reverse Electron Transport Extend Animal Lifespan

scientific article published on April 2016

Human mesenchymal stem cell-replicative senescence and oxidative stress are closely linked to aneuploidy

scientific article published on 27 June 2013

The function of the respiratory supercomplexes: the plasticity model

scientific article published on 22 December 2013

Defective extracellular pyrophosphate metabolism promotes vascular calcification in a mouse model of Hutchinson-Gilford progeria syndrome that is ameliorated on pyrophosphate treatment

scientific article published on 20 May 2013

Mitonuclear interactions: evolutionary consequences over multiple biological scales

scientific article

Mitochondrial respiratory-chain adaptations in macrophages contribute to antibacterial host defense.

scientific article published on 27 June 2016

The CoQH2/CoQ Ratio Serves as a Sensor of Respiratory Chain Efficiency.

scientific article published on 22 March 2016

ATP-Dependent Lon Protease Controls Tumor Bioenergetics by Reprogramming Mitochondrial Activity

Revisiting the mouse mitochondrial DNA sequence

scientific article

Isolation of mitochondria for biogenetical studies: An update

scientific article

Mitochondrial Respiration Controls Lysosomal Function during Inflammatory T Cell Responses.

scientific article published on 19 August 2015

Direct regulation of mitochondrial RNA synthesis by thyroid hormone.

scientific article

Allotopic expression of mitochondrial-encoded genes in mammals: achieved goal, undemonstrated mechanism or impossible task?

scientific article published on September 7, 2010

HIF-1α and PFKFB3 Mediate a Tight Relationship Between Proinflammatory Activation and Anerobic Metabolism in Atherosclerotic Macrophages

scientific article published on 16 April 2015

Supramolecular Organization of Respiratory Complexes.

scientific article

Mechanism of super-assembly of respiratory complexes III and IV.

scientific article published on 24 October 2016

An intragenic suppressor in the cytochrome c oxidase I gene of mouse mitochondrial DNA.

scientific article published on February 2003

Dysfunctional Coq9 protein causes predominant encephalomyopathy associated with CoQ deficiency

scientific journal article

Differences of sperm motility in mitochondrial DNA haplogroup U sublineages

scientific article published in December 2005

Identification of mitochondrial dysfunction in Hutchinson-Gilford progeria syndrome through use of stable isotope labeling with amino acids in cell culture

scientific article

ROS-triggered phosphorylation of complex II by Fgr kinase regulates cellular adaptation to fuel use

scientific article

Very rare complementation between mitochondria carrying different mitochondrial DNA mutations points to intrinsic genetic autonomy of the organelles in cultured human cells.

scientific article

Interplay between hepatic mitochondria-associated membranes, lipid metabolism and caveolin-1 in mice

scientific article published on 06 June 2016

Tissue-specific differences in mitochondrial activity and biogenesis

scientific article published on 07 October 2010

Nuclear transcription factors in mammalian mitochondria

scientific article

Priming of dendritic cells by DNA-containing extracellular vesicles from activated T cells through antigen-driven contacts.

scientific article published on 9 July 2018

Analysis of aminoacylation of human mitochondrial tRNAs

scientific article

Transient activation of mitochondrial translation regulates the expression of the mitochondrial genome during mammalian mitochondrial differentiation

scientific article published on May 1996

The synthesis of mRNA in isolated mitochondria can be maintained for several hours and is inhibited by high levels of ATP.

scientific article

The role of the mitochondrion in sperm function: is there a place for oxidative phosphorylation or is this a purely glycolytic process?

scientific article published on January 2007

Optic Atrophy 1 Is Epistatic to the Core MICOS Component MIC60 in Mitochondrial Cristae Shape Control

scientific article

Restoration of electron transport without proton pumping in mammalian mitochondria.

scholarly article

Cyclosporine A-induced nitration of tyrosine 34 MnSOD in endothelial cells: role of mitochondrial superoxide

scientific article published on 27 January 2010

A mitochondria-specific isoform of FASTK is present in mitochondrial RNA granules and regulates gene expression and function.

scientific article

Transmitochondrial embryonic stem cells containing pathogenic mtDNA mutations are compromised in neuronal differentiation.

scientific article published on 23 June 2009

List of works by José Antonio Enríquez

Mitochondrial cristae shape determines respiratory chain supercomplexes assembly and respiratory efficiency

Respiratory active mitochondrial supercomplexes.

Supercomplex assembly determines electron flux in the mitochondrial electron transport chain

Respiratory complex III is required to maintain complex I in mammalian mitochondria

Human mtDNA haplogroups associated with high or reduced spermatozoa motility

Differences in reactive oxygen species production explain the phenotypes associated with common mouse mitochondrial DNA variants

MtDNA mutation in MERRF syndrome causes defective aminoacylation of tRNA(Lys) and premature translation termination

NDUFA4 Is a Subunit of Complex IV of the Mammalian Electron Transport Chain

Mitochondrial Cristae: Where Beauty Meets Functionality.

Loss of mitochondrial protease OMA1 alters processing of the GTPase OPA1 and causes obesity and defective thermogenesis in mice

Induction of the mitochondrial NDUFA4L2 protein by HIF-1α decreases oxygen consumption by inhibiting Complex I activity.

Mitochondrial and nuclear DNA matching shapes metabolism and healthy ageing.

Isolation of biogenetically competent mitochondria from mammalian tissues and cultured cells

The deafness-associated mitochondrial DNA mutation at position 7445, which affects tRNASer(UCN) precursor processing, has long-range effects on NADH dehydrogenase subunit ND6 gene expression.

The mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episode syndrome-associated human mitochondrial tRNALeu(UUR) mutation causes aminoacylation deficiency and concomitant reduced association of mRNA with ribosomes.

Mitochondrial ROS Produced via Reverse Electron Transport Extend Animal Lifespan

Human mesenchymal stem cell-replicative senescence and oxidative stress are closely linked to aneuploidy

The function of the respiratory supercomplexes: the plasticity model

Defective extracellular pyrophosphate metabolism promotes vascular calcification in a mouse model of Hutchinson-Gilford progeria syndrome that is ameliorated on pyrophosphate treatment

Mitonuclear interactions: evolutionary consequences over multiple biological scales

Mitochondrial respiratory-chain adaptations in macrophages contribute to antibacterial host defense.

The CoQH2/CoQ Ratio Serves as a Sensor of Respiratory Chain Efficiency.

ATP-Dependent Lon Protease Controls Tumor Bioenergetics by Reprogramming Mitochondrial Activity

Revisiting the mouse mitochondrial DNA sequence

Isolation of mitochondria for biogenetical studies: An update

Mitochondrial Respiration Controls Lysosomal Function during Inflammatory T Cell Responses.

Direct regulation of mitochondrial RNA synthesis by thyroid hormone.

Allotopic expression of mitochondrial-encoded genes in mammals: achieved goal, undemonstrated mechanism or impossible task?

HIF-1α and PFKFB3 Mediate a Tight Relationship Between Proinflammatory Activation and Anerobic Metabolism in Atherosclerotic Macrophages

Supramolecular Organization of Respiratory Complexes.

Mechanism of super-assembly of respiratory complexes III and IV.

An intragenic suppressor in the cytochrome c oxidase I gene of mouse mitochondrial DNA.

Dysfunctional Coq9 protein causes predominant encephalomyopathy associated with CoQ deficiency

Differences of sperm motility in mitochondrial DNA haplogroup U sublineages

Identification of mitochondrial dysfunction in Hutchinson-Gilford progeria syndrome through use of stable isotope labeling with amino acids in cell culture

ROS-triggered phosphorylation of complex II by Fgr kinase regulates cellular adaptation to fuel use

Very rare complementation between mitochondria carrying different mitochondrial DNA mutations points to intrinsic genetic autonomy of the organelles in cultured human cells.

Interplay between hepatic mitochondria-associated membranes, lipid metabolism and caveolin-1 in mice

Tissue-specific differences in mitochondrial activity and biogenesis

Nuclear transcription factors in mammalian mitochondria

Priming of dendritic cells by DNA-containing extracellular vesicles from activated T cells through antigen-driven contacts.

Analysis of aminoacylation of human mitochondrial tRNAs

Transient activation of mitochondrial translation regulates the expression of the mitochondrial genome during mammalian mitochondrial differentiation

The synthesis of mRNA in isolated mitochondria can be maintained for several hours and is inhibited by high levels of ATP.

The role of the mitochondrion in sperm function: is there a place for oxidative phosphorylation or is this a purely glycolytic process?

Optic Atrophy 1 Is Epistatic to the Core MICOS Component MIC60 in Mitochondrial Cristae Shape Control

Restoration of electron transport without proton pumping in mammalian mitochondria.

Cyclosporine A-induced nitration of tyrosine 34 MnSOD in endothelial cells: role of mitochondrial superoxide

A mitochondria-specific isoform of FASTK is present in mitochondrial RNA granules and regulates gene expression and function.

Transmitochondrial embryonic stem cells containing pathogenic mtDNA mutations are compromised in neuronal differentiation.